CASE REPORT
Radiological features of perivascular epithelioid cell tumours (PEComas) in a paediatric patient – Case report
1
Medical University, Lublin, Poland
2
Medical University of Lublin, Poland
J Pre Clin Clin Res. 2022;16(1):9-12
KEYWORDS
TOPICS
ABSTRACT
Introduction:
Perivascular epithelioid cell tumour (PEComa) is a rare family of mesenchymal tumours composed of epithelioid cells. Due to its very rare occurrence, little information is available on the imaging characteristics of this type of lesion.
Case Report:
A 16-year-old patient was admitted for diagnosis of an incidentally found lesion of unclear origin on MRI of the lumbar spine. Targeted MRI revealed a pathological solid-cystic mass within the pelis, in the left rectovesical pouch, infiltrating the bladder wall. A biopsy of the tumour was performed. On histopathological examination, a PEComa tumour was diagnosed. Control examinations were performed. The tumour was treated with embolization, surgical resection and Sirolimus therapy.
Conclusions:
The tumour showed the characteristic features of PEC-oma on imaging studies reported in the literature. Radiological diagnosis is not fully specific, therefore histopathological examination is necessary for a definitive diagnosis
Perivascular epithelioid cell tumour (PEComa) is a rare family of mesenchymal tumours composed of epithelioid cells. Due to its very rare occurrence, little information is available on the imaging characteristics of this type of lesion.
Case Report:
A 16-year-old patient was admitted for diagnosis of an incidentally found lesion of unclear origin on MRI of the lumbar spine. Targeted MRI revealed a pathological solid-cystic mass within the pelis, in the left rectovesical pouch, infiltrating the bladder wall. A biopsy of the tumour was performed. On histopathological examination, a PEComa tumour was diagnosed. Control examinations were performed. The tumour was treated with embolization, surgical resection and Sirolimus therapy.
Conclusions:
The tumour showed the characteristic features of PEC-oma on imaging studies reported in the literature. Radiological diagnosis is not fully specific, therefore histopathological examination is necessary for a definitive diagnosis
Karska K, Kozioł I, Leśniewska M, Budzyńska J, Woźniak M. Radiological features of perivascular epithelioid cell tumours (PEComas) in
a paediatric patient – Case report. J Pre-Clin Clin Res. 2022; 16(1): 9–12. doi: 10.26444/jpccr/146536
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